Cochlear Implant Outcomes for Children With Auditory Neuropathy Spectrum Disorder Cochlear implantation is currently the intervention option of choice for many children with auditory neuropathy spectrum disorder (ANSD) who are unable to obtain benefit from conventional amplification. The aim of this study was to review the speech perception and language outcomes for children with ANSD who had received a cochlear ... Article
Article  |   September 2009
Cochlear Implant Outcomes for Children With Auditory Neuropathy Spectrum Disorder
Author Affiliations & Notes
  • Jaime Leigh
    Cochlear Implant Clinic, Royal Victorian Eye and Ear Hospital and Department of Otolaryngology, University of MelbourneMelbourne, Australia
  • Gary Rance
    Department of Otolaryngology, University of MelbourneMelbourne, Australia
  • Shani Dettman
    Department of Otolaryngology, University of MelbourneMelbourne, Australia
  • Richard Dowell
    Cochlear Implant Clinic, Royal Victorian Eye and Ear Hospital and Department of Otolaryngology, University of MelbourneMelbourne, Australia
  • © 2009 American Speech-Language-Hearing Association
Article Information
Hearing Disorders / Hearing Aids, Cochlear Implants & Assistive Technology / Articles
Article   |   September 2009
Cochlear Implant Outcomes for Children With Auditory Neuropathy Spectrum Disorder
SIG 9 Perspectives on Hearing and Hearing Disorders in Childhood, September 2009, Vol. 19, 75-84. doi:10.1044/hhdc19.2.75
SIG 9 Perspectives on Hearing and Hearing Disorders in Childhood, September 2009, Vol. 19, 75-84. doi:10.1044/hhdc19.2.75
Acknowledgments
The authors are grateful to the speech pathologists and audiologists of the Cochlear Implant Clinic, Royal Victorian Eye and Ear Hospital for their assistance collecting the speech perception and language data. Financial support for this work was provided by The University of Melbourne's Department of Otolaryngology and the Wagstaff Research Fellowship in Otolaryngology from The Royal Victorian Eye and Ear Hospital, Melbourne, Australia.
Abstract

Cochlear implantation is currently the intervention option of choice for many children with auditory neuropathy spectrum disorder (ANSD) who are unable to obtain benefit from conventional amplification. The aim of this study was to review the speech perception and language outcomes for children with ANSD who had received a cochlear implant and highlight specific clinical considerations for working with this population of children with hearing impairment who are being considered for implantation. Finds for the group of 17 children with ANSD using cochlear implants were compared to previously reported outcomes for children with sensori-neural (SN) type hearing loss using cochlear implants.

Two children, identified with cochlear nerve deficiency pre-operatively, received no useful auditory percepts from their cochlear implant and discontinued device use. The remaining children demonstrated speech perception and language outcomes comparable to those observed for SN hearing loss peers using cochlear implants.

This paper highlights a number of considerations for clinicians to be aware of and the importance of careful counseling pre-operatively regarding the potential for less-than-optimal outcomes, particularly for those children identified with cochlear nerve deficiency.

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